Journal of Shandong University (Health Sciences) ›› 2023, Vol. 61 ›› Issue (2): 65-71.doi: 10.6040/j.issn.1671-7554.0.2022.0352

• 临床医学 • Previous Articles     Next Articles

A case of non-tuberous sclerosis complex with giant angiomyolipoma of both kidneys treated with simultaneous resection and literature review

MA Chenbang1,2, GAO Pei1,2, CHANG Yao3, MAO Changlin1,2, CHEN Feng1,2, ZHU Kejia3, GUAN Yong3, LI Shanjun3, DING Sentai1,2,3   

  1. 1. Cheeloo College of Medicine, Shandong University, Jinan 250012, Shandong, China;
    2. Department of Urology, Shandong Provincial Hospital, Jinan 250021, Shandong, China;
    3. Department of Urology, Shandong Provincial Hospital Affiliated to Shandong First Medical University, Jinan 250021, Shandong, China
  • Published:2023-02-17

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Abstract: Objective To explore the accurate diagnosis and the safety and prognosis of simultaneous resection of giant angiomyolipoma of both kidneys. Methods Clinical data of a patient with giant angiomyolipoma of both kidneys were retrospectively analyzed. The 18-year-old female patient with body mass index(BMI)of 20.96 kg/m2 was admitted due to “palpable abdominal mass for 2 weeks”. Preoperative enhanced CT showed giant angiomyolipoma of both kidneys. Three-dimensional reconstruction of CT further clarified the tumor location, blood supply and other information. Results After exclusion of relevant contrain dications, bilateral resection was performed simultaneously with midline abdominal incision under general anesthesia. There were multiple angiomyolipomas around the kidneys. After dissociation, they were resected successfully. Routine pathological results indicated(bilateral)angiomyolipomas. During the 10-day postoperative hospitalization, no bleeding, renal failure or urinary leakage occurred. During the 12-month follow-up, no metastasis or recurrence was observed. Conclusion In addition to clinical symptoms and signs, gene detection, imaging reconstruction and other accurate diagnosis are necessary to formulate the surgical plan. Simultaneous resection of bilateral giant angiomyolipomas through one incision is safe and feasible.

Key words: Renal angiomyolipoma, CT three-dimensional reconstruction, Gene detection, Surgical treatment

CLC Number: 

  • R737.11
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