Abstract:

Objective   To analyze imaging findings and surgical therapy of Sturge-Weber syndrome, and to explore the effectiveness of multi-lobectomy for Sturge-Weber syndrome. Methods   The data of 3 Sturge-Weber syndrome patients (type I, 2 males and 1 female) were analyzed. Before surgery, all patients underwent CT and MRI scan and VEEG test and after surgery, they were followed up for 1 to 2 years. Results   In CT scans, the 3 patients manifested calcification in brain tissue. Abnormal blood vessels and cerebral atrophy were displayed in MRI imaging, and the disease area could be determined. 2 patients accepted tempro-occipital craniotomy, and the other patient accepted hemispherectomy. After 1 to 2 years follow-up, all patients had epilepsy release. Conclusion   Sturge-Weber syndrome can be determined by combining clinical manifestation and CT/MRI imaging. Surgical therapy should be taken as early as possible in patients with epilepsy. The total removal of lesions without adding functional deficiency can release the epilepsy seizure of SturgeWeber syndrome.

Key words: Sturge-Weber syndrome; Epilepsy; Surgical treatment; Imaging