山东大学学报 (医学版) ›› 2020, Vol. 58 ›› Issue (1): 91-93.doi: 10.6040/j.issn.1671-7554.0.2019.1228
• • 上一篇
王亚杰1,闻蓓2,施浩宇3,商亮1,董康迪1,李乐平1
WANG Yajie1, WEN Bei2, SHI Haoyu3, SHANG Liang1, DONG Kangdi1, LI Leping1
摘要： 目的 本文旨在探讨合并血友病的外科患者围手术期管理。 方法 分析一名胃癌合并轻型血友病A的患者术后出血的临床特点、诊断及治疗过程,同时对围手术期合并血友病的处理要点进行文献复习。 结果 通过组织多学科会诊,深入了解病情,血液检查发现患者凝血因子Ⅷ活性降低,确诊该患者合并轻型血友病A。并对患者进行输注重组凝血因子Ⅷ治疗,其出血症状得到治愈。 结论 对于血友病患者的围术期管理,目前替代疗法是最主要的治疗方案。首选重组FⅧ制剂,并根据手术类型、损伤程度等,适当延长替代治疗时间。患者应在血友病中心进行登记,进行长期随访。
中图分类号:
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