MRKH综合征相关腹股沟子宫疝修补术后腹壁瘢痕子宫内膜异位症1例报道并文献复习

doi:10.6040/j.issn.1671-7554.0.2021.1259

摘要/Abstract

摘要： 目的为临床工作处理MRKH综合征相关腹股沟子宫疝修补术后腹壁瘢痕子宫内膜异位症相关病例提供参考。方法回顾了1例于山东大学齐鲁医院住院治疗的MRKH综合征相关腹股沟子宫疝修补术后腹壁瘢痕子宫内膜异位症患者的临床资料,并对相关文献进行复习。结果该患者入院后完善相关辅助检查,行腹腔镜下双侧始基子宫切除+右侧输卵管切除+盆腔粘连松解术+经腹腹壁切口子宫内膜异位病灶切除术,术后给予6周期注射用醋酸亮丙瑞林缓释微球3.75 mg皮下注射,效果好。结论对于有症状的MRKH综合征患者,可行手术治疗改善患者症状并提高生活质量。子宫内膜异位症相关疼痛可行手术切除或破坏病灶,缓解疼痛,且需终身管理。

关键词: 生殖系统畸形, MRKH综合征, 始基子宫, 子宫内膜异位症, 腹股沟疝

Abstract: Objective To provide reference for the clinical treatment of cases with MRKH syndrome-related abdominal scar endometriosis after inguinal uterine hernia repair. Methods The clinical data of a patient with MRKH syndrome-related abdominal scar endometriosis after inguinal uterine hernia repair and relevant literature were reviewed. Results After admission, the patient completed relevant auxiliary examinations, underwent laparoscopic bilateral primordial hysterectomy, right salpingotomy, pelvic adhesionolysis, transabdominal abdominal incision endometriosis lesion resection. After surgery, she received subcutaneous injection of leuprorelin acetate sustained-release microspheres of 3.75 mg for 6 cycles, and the effect was satisfactory. Conclusion For patients with MRKH syndrome, surgical treatment is feasible to improve the symptoms and quality of life. Pain associated with endometriosis may be relieved by surgical resection or destruction of the lesion, but lifelong management is required.

Key words: Malformation of the reproductive system, MRKH syndrome, Primordial uterus, Endometriosis, Inguinal hernia

中图分类号:

R711.1

陈忠绍,褚然,李明宝,张向宁. MRKH综合征相关腹股沟子宫疝修补术后腹壁瘢痕子宫内膜异位症1例报道并文献复习[J]. 山东大学学报 (医学版), 2022, 60(5): 114-117.

CHEN Zhongshao, CHU Ran, LI Mingbao, ZHANG Xiangning. MRKH syndrome-related abdominal scar endometriosis after inguinal uterine hernia repair: a case report and literature review[J]. Journal of Shandong University (Health Sciences), 2022, 60(5): 114-117.

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